Seznec H

Seznec H

French National Centre for Scientific Research - Paris / France
Others
AD Scientific Index ID: 4728245
Centre National de la Recherche Scientifique CNRS
person_outline Seznec H's MOST POPULAR ARTICLES
1-) Mice transgenic for the human myotonic dystrophy region with expanded CTG repeats display muscular and brain abnormalities H Seznec, O Agbulut, N Sergeant, C Savouret, A Ghestem, N Tabti, ... Human Molecular Genetics 10 (23), 2717-2726, 2001 2562001
2-) Friedreich ataxia: the oxidative stress paradox H Seznec, D Simon, C Bouton, L Reutenauer, A Hertzog, P Golik, ... Human molecular genetics 14 (4), 463-474, 2005 2342005
3-) Friedreich ataxia mouse models with progressive cerebellar and sensory ataxia reveal autophagic neurodegeneration in dorsal root ganglia D Simon, H Seznec, A Gansmuller, N Carelle, P Weber, D Metzger, ... Journal of Neuroscience 24 (8), 1987-1995, 2004 2162004
4-) Transgenic mice carrying large human genomic sequences with expanded CTG repeat mimic closely the DM CTG repeat intergenerational and somatic instabilityH Seznec, AS Lia-Baldini, C Duros, C Fouquet, C Lacroix, ...Human molecular genetics 9 (8), 1185-1194, 20002132000
5-) Idebenone delays the onset of cardiac functional alteration without correction of Fe-S enzymes deficit in a mouse model for Friedreich ataxiaH Seznec, D Simon, L Monassier, P Criqui-Filipe, A Gansmuller, P Rustin, ...Human molecular genetics 13 (10), 1017-1024, 20041622004